Minimally Invasive Mitral Valve Repair in a Woman with Marfan Syndrome and Type B Dissection

نویسندگان

  • Mi Hee Lim
  • Hyung Gon Je
  • Sang Kwon Lee
چکیده

We report the case of a patient with mitral regurgitation complicated by type B dissection and Marfan syndrome (MFS) who was managed successfully with minimally invasive mitral valve repair. Without type A aortic dissection or aortic root dilation, MFS patients may develop mitral valve regurgitation, as in this case, and need valve surgery to improve their symptoms and long-term survival. However, it is not clear that a full sternotomy and prophylactic aortic surgery are necessary. Although retrograde perfusion to the dissected aorta is controversial, our approach minimizes the risk of future anticipated aortic surgery in MFS patients.

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عنوان ژورنال:

دوره 51  شماره 

صفحات  -

تاریخ انتشار 2018